Search on: MITOCHONDRIAL TRIFUNCTIONAL PROTEIN, ALPHA SUBUNIT 
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Descriptor English:   Mitochondrial Trifunctional Protein, alpha Subunit 
Descriptor Spanish:   Subunidad alfa de la Proteína Trifuncional Mitocondrial 
Descriptor Portuguese:   Subunidade alfa da Proteína Mitocondrial Trifuncional 
Tree Number:   D08.811.520.241.300.250.249.500
D08.811.641.765.200
D08.811.682.047.820.150.707.249.500
D12.776.543.602.200
D12.776.575.765.200
Definition English:   The alpha subunit of mitochondrial trifunctional protein. It contains both enoyl-CoA hydratase activity (EC 4.2.1.17) and long-chain-3-hydroxyacyl-CoA dehydrogenase activity (EC 1.1.1.211). There are four of these alpha subunits in each mitochondrial trifunctional protein molecule. 
History Note English:   2014 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DF deficiency
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Record Number:   55286 
Unique Identifier:   D063992 

Occurrence in VHL:
 

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